International Journal of Academic Research and Development

International Journal of Academic Research and Development


International Journal of Academic Research and Development
International Journal of Academic Research and Development
Vol. 3, Issue 3 (2018)

Clinicoradiological profile of Hirayama disease: An experience from a tertiary care centre in Kerala


Muhammad PK, Vishal VP, Shaji CV, Kabeer KA, Nikhil G, Meenakumari S

Background: Hirayama disease (HD) is a benign disease characterized by unilateral or asymmetric distal upper limb weakness and wasting. Objective: To study the clinical and radiological profile of patients with HD. Materials and Methods: Clinicoradiological evaluation were done in a total of 8 patients presented with insidious‑onset hand wasting from March 2015 to June 2017. Results: All were males, mean age of onset of 19.5 years. 7 out of 8 (87.5%) had asymmetric wasting and weakness. All (100%) had oblique amyotrophy, two (25%) had cold paresis, four (50%) had minipolymyoclonus, and 3 (37.5%) had history of trauma to cervical region. Flexion MRI contrast study showed enchancing epidural crescent with anterior displacement of posterior cervical dura in all patients. Conclusion: Though Dynamic contrast MRI is characteristic, routine studies have a high predictive value for diagnosis. Prompt diagnosis is important to institute early collar therapy.
Pages : 172-179 | 565 Views | 187 Downloads